[ a] [ ] ( 15) 2005( 17) 2006( 18) [ ( )] [ b] 1996( 8) 1998( 10) 2003( 15) 2006( 18) [ c] [ ] 24

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1 [ a ( :2-4)] [ ( :2-4)] [ ( :2-4)] 1955( 30) 1972( 47) ( 49) () 1996( 8) [ ( :2-4)] 1998( 10) 1992( 4) 2001( 13) 1996( 8) 2000( 12) 23

2 [ a] [ ] ( 15) 2005( 17) 2006( 18) [ ( )] [ b] 1996( 8) 1998( 10) 2003( 15) 2006( 18) [ c] [ ] 24

3 [ b] [ ] 37(10) /5 1/3 8 [ ] 5(2) p<

4 p<0.1 [ ] 3(1) Cronbach r=-0.25 p r=-0.24 p r=-0.32 p 0.05 [ a] Quality of Life 5(3) [ a] Cronbach 0.88 p<0.1 r=0.25 p=0.08 [ b] 26

5 ALS - 6(2) % % % p<0.01 p< [ a] 6(3) [ a] [ b] 27

6 5(1) p< p<0.01p<0.05 p<0.05 [] 36(5) [ ] 13(6) (72 ) 7 (28 ) (24 ) 19 (76 ) 21 (84 ) (48%) 24 28

7 3 (12%) 10 (40%) 25 (100%) 13 52% [ 2008] 23() Zarit p<0.05 [ ] 50(6) ALSFRS ALSFRS ALSFRS J-ZBI r= p SF-36 ALSFRS p=0.01 [ ] 29

8 [ a] [ ] [ b] - 6(2) [ a( )] 64(12)

9 [ ] ( ) 1(1) (1) [ a] ( ) [ b] ( ) 12(2) (4)

10 [ b] 100% [ c] [ ] 8(3) [ ( )] 10(3)

11 [ ] [ ] [ ]

12 34

13 35

14 [ ] [ ] [ ] [ ] [ ( :2-4)] [ ( )] [] [ ] [ ] [ ( :1-1)] [] [ ] 36

15 [ ] [ ] [ ] [ ] [ ] [ ] [ ] [ ] [ ] [ ] 37

16 [ a] 8(4) [ ] 8(3) [ ] 51(4) [ ] [ a] [ ] Modern Physician 28(5) [ b] [ c] [ ] 64(12) [ b] 8(1) [ ] 8(4) [ ] 37(10) [ ] 5(2) [ a] 3(1) [ b] Quality of Life 5(3) [ a] ALS - 6(2) [ b] ALS 6(3) [] 38

17 5(1) [ ] 36(5) [ a] ALS 13(6) [ ] 23() [ ] QOL 50(6) [ a] ALS 10(3) [ ] 9(1) [ b] 9(3) [ a] [ ] 64(12) [ a] 1(1) [ b] 3 1(1) [ b] 12(2) [ c] 57(4) [ ] [ ] [ ] 10(3) [ ] 5(6) [ ] 14(10)

18 [ ] Medical Rehabilitation [ ] [ ] 3(1) [ ] [] 29(1) [ ] 18(9) [ ] 9(4) [ ] Medical Rehabilitation [] 46(1) [ ] [ ] [ ] 64(12) [ ] ALS Modern Physician 22(5) [ ] 33( 2) [ ] 18(1) [ ] ALS 9(1) [ ] 18(10) [ ] 18(11) [ ] 50(1) [ ]

194621 22 50.06 53.96 90.00 28 87.14 85.00 80.00 75.00 70.00 22 53.96 28 80.75 65.00 60.00 55.00 22 50.06 50.00 Quality of Life !! 281026 281026 -6,500-5,500-4,500-3,500-2,500-1,500-500 500 1,500 2,500-6,401-1,281-3,565-2,154-2,265-2,027-1,869-1,657

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