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3 20 Contents 1 IgE 2 2 Netherton 6 3 WiskottAldrich trna Schnitzler Sjögren 41 vii
4 19 BlochSulzberger GianottiCrosti StevensJohnson Column Sézary 82 viii
5 Contents 20 Kindler Wells Bloom Cockayne RothmundThomson SjögrenLarsson 26 Rud Blaschko Conradi 118 ColumnConradi DorfmanChanarin Netherton ix
6 31 BlochSulzberger PapillonLefèvre Vohwinkel KID Bazex SAPHO FavreRacouchot Waardenburg 39 Vogt x
7 Contents 40 HermanskyPudlak ChédiakHigashi Werner HutchinsonGilford EhlersDanlos Marfan GrönbladStrandberg ZinsserColeEngman Kindler RothmundThomson 208 xi
8 50 SturgeWeber KlippelTrenaunay KasabachMerritt KasabachMerritt Maffucci CrowPOEMS OslerWeberRendu StewartTreves PeutzJeghers 244 xii
9 Contents 60 LaugierHunzikerBaran CronkhiteCanada LEOPARD LeserTrélat MuirTorre BirtHoggDubé BrookeSpiegler Gardner GorlinGoltz trigeminal trophic syndrome Münchhausen References 299 Index 338 xiii
10 2 Netherton 29 Netherton Nethertons syndrome Comèl-Netherton syndrome OMIM LEKTISPINK5 HE 6
11 2 Netherton Netherton 7
12 1 8
13 2 Netherton Netherton 2 Netherton LEKTI 9
14 Netherton 10
15 2 Netherton 11
16 TEL ISBN Published by Nakayama Shoten Co., Ltd. Printed in Japan
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i 1 1 1 2 3 5 5 6 7 9 10 11 13 13 14 15 15 16 17 18 20 20 20 21 22 ii CONTENTS 23 24 26 27 2 31 31 32 32 33 34 37 37 38 39 39 40 42 42 43 44 45 48 50 51 51 iii 54 57 58 60 60 62 64 64 67 69 70 iv 70 71
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