小児問題

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1 (glioma)(meningioma) (pituitary adenoma) (J-95 (J-4) angio (J-185) (J-173) Schwann MRI. ( ) PRL PRL GH V1 V2 V3 X X X

2 Rinne test: 4-5cm test(+) Weber test: PRL Rathke s pouch() ( ) Willis 3 6

3 1. Tonic neck reflex 2. 5~6 4~6 9 6~8 2~3 1 Moro 4 1 2~ CT (1)(2) 5. (1)Monro (2)Luschka Magendie Monro 4 Parinaud sign 1

4 a)v-p shunt b)v-a shunt c)l-p shunt CT CT

5 13. 3 alobar type 1 semilobar type lobar type Dandy-walker Chiari 2 Apert 16. Verga Verga 17. Dandy-walker Dandy-walker Magendie Luschka 4 (1) (2) 4 Dandy-walker Magendie 4

6 Chiari Chiari 21. Chiari Chiari Chiari Crouzon 27. Apert 28. STEP

7 [ ] [ ] [ kantan ] [ ] 2 fronto-orbital advancement Crouzon 50%

8 Apert 29. Arnold-Chiari 30. Klippel-FeilArnold-Chiari 31. Klippel-Feil 2 Klippel-Feil von Recklinghausen I II 100% I von Recklinghausencafé au lait II c.f. Scwan cell Scwan cell West

9 36. Sturge-Weber 37. von Hippel-Lindau von Hippel-Lindau 38. Galen Galen Galen Galen 3 1 Galen 2 3 AV SAH

10 Jacob 12. tethered cord syndrome Jacoby (a)x (b) (b)

11 4. (Th1 L3) Artery of Adamkiewicz 3 ~ Adamkiewicz AAA

12 6. anterior spinal 7. central cord 8. posterior spinal 9. Brown-Sequard s syndrome

13 10. fasciculation, fibrillation? Babinski reflex? fasciculation, fibrillation? Babinski reflex? fasciculation, fibrillation Babinski reflex fasciculation, fibrillation or Babinski reflex(-) 11. Chiari type C5 C6 Horner 15. intramedullary AVM (nidus) nidus perimedullary AVF myelopathy dural AVF

14 (1)(2) (3) (1) (2) (3) 18. sacral sparing sacral sparing 19. 5% 25% 1 10% 45%40%15% 20. X

15 decompression realignment stabilization (A) i) ii) (B) i) 2 ii) ii-a) ii-b) (C) Spinal shock Spinal shock

16 STEP HP up to date

02-56fl]’_„o68fl]”îá⁄-…v…“…O…›…•

02-56fl]’_„o68fl]”îá⁄-…v…“…O…›…• 8:55 9:00 19:00 9:32 29:32 10:04 AVF10:04 10:28 AVM10:28 11:00 111:00 11:24 211:24 11:48 12:00 13:10 13:10 13:20 13:20 14:20 14:20 14:30 14:30 14:46 14:46 15:10 115:10 15:42 215:42 16:14 16:14 9:00 9:24

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