Full Haemophilia Translation: (2000), Hemophilia 6, (Suppl.1), of Georgia 84-93 Hemophilia of Georgia 1 Treatment of Hemophilia Monograph Series, Number 14. World Federation of Hemophilia: 1998. Protocols for the Treatment of Hemophilia and von Willebrand Disease is currently being revised by Hemophilia of Georgia and the haemophilia treatment centres of Georgia. For more information on the revised version, please contact Hemophilia of Georgia, 8800 Roswell Road, Suite 170, Atlanta, Georgia 30350, U.S.A. 3 Professor C. K. Kasper, MD A B Table 1 X VIIIIX A 1 1 B 3 5 1 VIII von Willebrand DNA DNA DNA 9 11 12 15 VIII B IX IX IX 6 Fig. 1 32
von Willebrand 1. 2 (i) (ii) 2. (i) 23G 25G (ii) (iii) 3 5 3. Table 2 + 4. 3 5 5. 1980 1. Kogenate, Bioclate, Helixate, Recombinate; 2. AHF-M, Hemofil M, Monoclate P; 3. VIII Humate P, Alphanate von Willebrand Koate HP, Profilate SD 33
Full Translation: Hemophilia of Georgia HIV 300 1,600 1 VIII 2% 8 12 0.5 45kg 40 % 0.5 900 Table 3 VIII 1 3ml 1 100 1 4 5 /kg/h 100% VIII VIII 12 12 1 60 100 VIII 34
von Willebrand DDAVPStimate VIII5% DDAVP DDAVP VIII VIII 2 3 DDAVP DDAVP VIII DDAVP 0.3µg/kg 30 50ml 15 30 30 60 VIII 2 3 Stimate 15von Willebrand (type 1) 5 Stimate von Willebrand DDAVP 1 1 Na ε -(Amicar EACA) 50 100mg/kg 1 4 6 7 10 24g/day Cyklokapron, TECA TA 1 25mg/kg 1 3 8 10 Amicar IX 1991 2 1. IX Alphanine SD, Mononine 2. IX Konyne 80, Bebulin HIV U.S.A. the Medical and Scientific Advisory Council (MASAC) IX Alphanine SD, MononineDIC IX Konyne 80, Bebulin IX B DIC IX IX 300 1,200 1 IX 1% 18 24 45kg 40 % 1,800 Table 3 IX 1 3ml B 35
Full Translation: Hemophilia of Georgia IX IX 15% 15ml/kg FFP IX 1. X 2. 40% 60 80% 3. 2 12 A 24 B 4. 5. 6. 3 7. Table 2 1. 2. 40% 3. 2 24 36
von Willebrand 1. 2. A 80 100% B 60 80% 48 96 A B 30 60% 3. 4. CT 5. 1. 2. A 80 100% B 60 80% 2 3 A 50% B 30% 3. CT MRI 4. 5. HIV HIV 1. A 80 100% B 60 80% A 50% B 30% 2. CT MRI 3. 1. 2. A 80 100% B 60 80% A 50% B 30% 3. 4. 5. 6. VIII Amicar EACA 1. 2. A 80 100% B 60 80% A 50% B 30% 37
Full Translation: Hemophilia of Georgia 1. 2. A80 100% B 60 80% 3. 1 2 2 5 4. 5. 4% 6. EACA 1. 2. 1.5 3. A 50% B 40% 4. 1. IX 2. VIIIAmicar EACA Amicar EACA 3. 4. 5. Avitene Thrombin 6. 1. 2. 20 3. NeoSynephrine 0.5 1% 1. 2. 3. 1. 2. 3. A50% B 40% von Willebrand vwd X vwd von Willebrand vwf VIII von WillebrandVIII von Willebrand 38
von Willebrand vwd Type 1 vwd vwd Type 2 vwd Type 2 vwd Type 2B Type 3 vwd vwf FVIII A Type 1 vwd DDAVP DDAVP Type 2A Type 2B Type 3 vwd DDAVP Type 2B DDAVP Type 3 vwf VIII vwf Humate-P Alphanate Koate HP vwf VIII vwf vwd HIV A vwf Type 1 Type 2A DDAVP DDAVP 1. 2. A 50% B40% 3. A 50% B 40% IX VIII Amicar EACA) 24Amicar EACA) 50 100mg/kg 1 4 6 7 10 24g/day 25mg/kg 1 3 8 10 Amicar EACA 4. Amicar 5. 6. 3 10 7. Avitene 39
Full Translation: Hemophilia of Georgia 8. 9. 1. 2. 3. A 80 100% B 60 80% A 50% B 30% 4. 5 7 10 14 6 1. 5 2. MMR 3. HIV 4. A B A B B 40
von Willebrand 1985 HIV HIV 1985 HIV HIV HIV Pneumocystis carinii HIV 1985 HIV 1985 HIV HIV HIV HIV B 1. 2. Benadryl 3. 41
Full Translation: Hemophilia of Georgia 42