70% ADCA 28% SCA6 30% MJD 30% DRPLA 13% 20% SCA1 4% SCA2 3% RCA 2%
537 25
T2
C3 C6) LCL MRI
OB ph3 ph9
60/40/20mg/ 1000mg/ 3 500mg/ 6
1000mg/ 3 6/ 2 1 2 3
50 25 0 75 100 % 100 33 67 75 80 84 6
0 10 20 24 21 / 24 (88%) 15 / 21 (71%) MS 24 21 88% 3 LCL: Long Cord Lesion 15 / 21 71% AQP4 1 2
MS Goodkin, D., et al.: Neurology 42: 859-863, 1992 Kurtzke, J. F.: Neurology 33: 1444-1452, 1983
MRI MRI CIS RRMS SPMS McDonald MS
β 2 β β β 3
4 APP)
5% 95% ε 5 6
7 n (n-3 PUFA) AD
8 β
9 10 Integrated treatment approach, Combination therapy
1 MRI
3 MIBG 4
3 MAO-B
4 7
4 a 1 1 1 4 b 1 1 1
5 10