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A Case of Pseudohypoparathyroidism with Cutaneous Ossification Sayoko Ohno, Tadashi Yokoo, Miyuki Ohta, Masamitsu Yamamoto, Yoshikazu Morita and Kiichiro Danno Department of Dermatology, Tenri Hospital Hitoshi Ishii Department of Endocrinology, Tenri Hospital Key words: pseudohypoparathyroidism-albright's hereditary osteodystrophy- Pseudopseudohypoparathyroidism-cutaneous ossification A 21-year-old woman with hard subcutaneous nodules on her left forearm visited Tenri Hospital for the tetanic convulsion. Examination revealed hypocalcemia, hyperphosphatemia and no phosphate excretion response to PTH. She was diagnosed as pseudohypoparathyroidism (PH). The histology of a subcutaneous nodule showed cutaneous ossification. She was a short, round-faced and stocky woman. Her hands and feet were stubby. These appearances, so-called Albright's hereditary osteodystrophy (AHO), including cutaneous calcification and ossification are also known to be the features of pseudo pseudohypoparathyroidism (PPH), in which serum Ca and P levels are normal. Therefore cutaneous calcification and ossification cannot be explained by hypocalcemia and hyperphosphatemia. These physical characteristics are