WBC Table1 Laboratoryfindings 9,000/μl RBC 396 10 4 /μl Hb 9.8 g/dl <catecholamine> adrenaline 46 pg/ml (<100) Ht 31.9% noradrenaline 144 pg/ml Plt 34.7 10 4 /μl (100~450) dopamine 9pg/ml CEA <0.5ng/ml (<20) CA19 9 BUN Cr TP TB GOT GPT 14U/ml 12.0mg/dl adrenaline 0.98mg/dl 5.50g/dl 0.20mg/dl 18IU/l 16IU/l <urinarycatecholamine> noradrenaline dopamine urinaryvma 11.8 μg/day (3.0~15.0) 97.6 μg/day (26.0~121.0) 1,399.9 μg/day (190.0~740.0) 4.0 mg/day (1.3~5.1) <adrenalcortexhormone> ACTH DHEA-S 53.4 pg/ml (7.4~55.7) 1,350 ng/ml (830~3,960)
Fig.1 Abdominalcomputedtomographyrevealed awel-defined largetumoroccupying entireabdominalcavity. Fig.3 Balium enemaexaminationshowedcompressionofthetransversecolonbythetumor. Fig.2 A:A T1-weighted coronalmagneticresonanceimage(mri)revealedthetumorwithlow intensity in the abdominalcavity.b:a T2- weighted coronalmrirevealed thetumorwith highintensityintheabdominalcavity.
Fig.4 Angiography revealed the feeding artery from theleftrenalartery(arrow). Fig.5 Intraoperativeview:thelargetumorarisen from retroperitoneum occupyingentireabdominal cavity.
Fig.6 A:Theresectedspecimenshowedasolid,encapsulatedtumorwith hemorrhage,measuring395 250 170mm insizeandweighed7.5kg.b: Cutsurfaceofthespecimenwasgray-whitecolor,revealingcentralnecrosisfocus. Fig.7 Histopathologicalfindings:A:The tumor composedof paternless arrangementofspindle celsseparatedbydensebundlesofcolagen(he, 200).B:AlthetumorcelswerestronglyreactiveforCD34immunochemicalstaining( 200).C: TumorcelswerepositiveforBcl-2( 200).D:TumorcelswerepositiveforMIC-2( 200).
Table2 Reportedcasesoflargesolitaryfibroustumorsweighedover1kg Author Year Age/Sex Location Symptom Size Weight Immmunohistochemical Prognosis Briseli 15) 1981 47Female Diaphragmaticpleura Free 33cm 3,260g Flemming 16) 1996 53Female Pericardium Weightloss 18cm 2,800g cytokeratin(-) Guglielmi 17) 1998 61Female Liver Abdominalfulness 20 16 10cm 2,850g CD34(+)S-100(-) Alive6years Hirai 18) 1998 55Female Diaphragmaticpleura Consciousloss 25 20 14cm 3,000g cytokeratin(+) Kiriyama 19) 1998 51Female Mediastinum Dyspnea 27 21 17cm 2,100g Hagiwara 20) 1999 63Female Diaphragmaticpleura Dyspnea 25 20 12cm 2,500g Mori 21) 1999 58Female Lefthemithorax Consciousloss 24 16 9.5cm 2,900g Kondo 22) 2000 38Female Massoftheback 21 11 7cm 1,750g vimentin(+)cd34(-) cytokeratin(+)s-100(+) Alive5years Takemoto 23) 2000 48Female Free 19.5 16.5cm 2,056g Alive3years Heianna 24) 2000 19Male Diaphragmaticpleura Free 23 14 14cm 2,340g CD34(+)cytokeratin(+) Kim 25) 2001 64Female Diaphragmaticpleura Dizziness 20 17 4cm 1,150g Alive2years cytokeratin(-) Kim 25) 2001 71Female Diaphragmaticpleura Dysarthria 14 12 10cm 1,180g Alive10months Nunoi 26) 2001 70Male Dyspnea 18 17 15cm 3,200g CD34(+) Alive2years Sudou 27) 2003 64Female Free 16 13 8cm 1,150g Hashimoto 28) 2004 81Female Chestdiscomfort 24 20 5.5cm 1,170g S-100(-)bcl-2(-) Kunieda 29) 2004 53Male Retroperitoneum Painlessswelingof theabdomen 14 13 10cm 1,200g Alive3years Vennarecci 30) 2005 65Male Liver Abdominaldiscomfort 30 28 14cm 4,725g Alive30months Presentcase 47Male Retroperitoneum Abdominalfulness 39.5 25 17cm 7,500g CD34(+)bcl-2(+)MIC-2(+) Alive18months