A Clinical and Electroencephalographic Study of Myoclonic Epilepsies in Infancy and Early Childhood Part 1. On the Classification Key Words: myoclonic epilepsy, classification, infancy and early childhood, prognosis, syndrome. Hirokazu Oguni, Yukio Fukuyama Department of Pediatrics, Tokyo Women's Medical College
Fig.1 Typical examples of generalized bilateral synchronous epileptic discharges recorded during sleep in patients with myoclonic seizures Type 1=Generalized bilateral synchrc nous multiple spikes and waves complexes Type 2=Generalized bilateral synchronous multiple sharp and slow waves complexes Type 3=Generalized burst of irregular multiple spikes associated with wave
Table 1 Subclassification of 149 patients with myoclonic seizures according to the clinial and electroencephalographic features The remaining 12 patients could not be classified. Abbreviations are as follows; Genetics=% of patients with positive family history of febrile convulsion or epilepsy BME=Benign myoclonic epilepsy in infants (Dravet, C) CMC=Cryptogenic myoclonic epilepsy of childhood (Aicardi, J) MEC=Myoclonic epilepsy of childhood (Jeavons, PM) SME=Severe myoclonic epilepsy in infants (Dravet, C) MAE=Myoclonic astatic epilepsy of early childhood (Doose, H)
lepsy of childhood (Aicardi)1 `3), benign myoclonic epilepsy in infants (Dravet)9), myoclonic astatic epilepsy of early childhood (Doose)6,7) Ì
severe myoclonic epilepsy in infants (Dravet10)) epilepsy with non-progressive encephalopathy jerks, myoclonic petit-mal, cryptogenicc myoclonic epilepsy of childhood, generalized epilepsy
mary generalized myoclonic astatic petit mal, myoclonic astatic epilepsy of early childhood
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